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伴空洞;D:左肺囊性改变;E:左肺胸腔积液伴囊性改变;F:左肺囊性改变较前吸收三、诊断系统性红斑狼疮合并ANCA血管炎,抗肾小球基底膜抗体阳性,合并了肺部感染+泌尿系感染四、治疗患者临床表现为肾病
D:下腔静脉肝后段缺失;E:胰腺短小;F:奇静脉扩张图2 患者腹部CT及胆道MRCP成像 A、B:肝内胆管串珠样改变;C:胆总管扩张;D:胆道水成像4.基因检测全外显子基因检测:患者本人及儿子未检出